Familial ventricular tachycardia: a report of four families.
نویسندگان
چکیده
Four cases of familial ventricular tachycardia are presented. In each family the proband was an adolescent girl. Twelve members in the four families were affected and all were female. The clinical and electrocardiographic features were relatively constant within each family but there were striking differences between families. These differences argue against a common electrophysiological or pathophysiological basis for the ventricular tachycardia.
منابع مشابه
Prospective evaluation of relatives for familial arrhythmogenic right ventricular cardiomyopathy/dysplasia reveals a need to broaden diagnostic criteria.
OBJECTIVES We sought to ascertain the prevalence and mode of expression of familial disease in a consecutive series of patients with arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D). BACKGROUND Autosomal-dominant inheritance is recognized in ARVC. The prevalence and mode of expression of familial disease in consecutive, unselected families is uncertain. METHODS First- and ...
متن کاملFamilial form of arrhythmogenic right ventricular dysplasia presenting with recurrent ventricular tachycardia.
We report on a 48-year-old man who presented with recurrent sustained monomorphic ventricular tachycardia, which resulted in syncope on one occasion. Subsequent investigation confirmed the diagnosis of arrhythmogenic right ventricular dysplasia. Familial screening for the disease was conducted using 12-lead electrocardiography, signal-averaged electrocardiography, and magnetic resonance imaging...
متن کاملCardiac abnormalities in familial palmoplantar keratosis.
Cardiac abnormalities were identified in patients with familial palmoplantar keratosis. All of them were descended from families on the Greek island of Naxos. Four families were studied and nine cases of palmoplantar keratosis were identified; seven of them showed symptoms and signs of heart disease. Cardiomegaly on chest x ray and electrocardiographic abnormalities were common findings. Three ...
متن کاملSudden unexplained death: heritability and diagnostic yield of cardiological and genetic examination in surviving relatives.
BACKGROUND Sudden death mostly follows from cardiac disorders that elicit lethal ventricular arrhythmias. In young individuals, it often remains unexplained because history and/or postmortem analysis are absent or provide no clue. Because such sudden unexplained deaths (SUDs) may have heritable causes, cardiological and genetic assessment of surviving relatives of SUD victims may reveal the und...
متن کاملSudden cardiac death with autopsy findings of uncertain significance: potential for erroneous interpretation.
BACKGROUND The sudden death of young individuals is commonly attributed to inherited cardiac disorders, and familial evaluation is advocated. The identification of pathognomonic histopathologic findings, or the absence of cardiac pathology (sudden arrhythmic death syndrome [SADS]) at postmortem, directs familial evaluation targeting structural disorders or primary arrhythmogenic syndromes, resp...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
- British heart journal
دوره 63 3 شماره
صفحات -
تاریخ انتشار 1990